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Jumbo and Nonye-Enyidah

Greener Journal of Medical Sciences

Vol. 11(2), pp. 246-248, 2021

ISSN: 2276-7797

Copyright ©2021, the copyright of this article is retained by the author(s)

https://gjournals.org/GJMS

 

 

 

 

 

 

Giant Omphalocele With Multiple Major Structural Anomalies In A Primipara At 25 Weeks Gestation: A Rare Case Report.

 

 

Awopola Ibiebelem Jumbo*; Esther Ijeoma Nonye-Enyidah

 

 

Department of Obstetrics and Gynaecology, Rivers State University Teaching Hospital, Port Harcourt, Nigeria.

 

 

ARTICLE INFO

ABSTRACT

 

Article No.:112121129

Type: Research

 

 

Background: Omphalocele is a major congenital anterior abdominal wall defect. It is often associated with other congenital anomalies that contribute to an increase in perinatal morbidity and mortality. The diagnosis could be made earlier in pregnancy with routine antenatal ultrasonography or prenatal diagnosis. Following this, termination may be offered.

Objective: To report a case of omphalocele with major structural abnormalities in a primipara at 25 weeks gestation.

Methods: The case note of the patient and how she was managed were reviewed. A relevant review of the literature on the subject was also done.

Case report: Mrs OJ was a 25year-old primipara who presented for booking at 25 weeks of gestation. she had an ultrasound scan at booking and the foetus was incidentally diagnosed as a case of omphalocele with associated major structural anomalies. She had not received folic acid in the index pregnancy and had no other risk factors. The pregnancy was terminated with misoprostol tablets following counselling. The baby was a fresh stillborn with giant omphalocele associated with gastrointestinal, renal and limb abnormalities.

Conclusion: The incidence of omphalocele could be reduced by routine use of folic acid around the time of conception and in the first trimester. However, most women in developing countries book late in pregnancy when prevention is not possible. There is a need to educate women on early booking, improve access to antenatal care and supplement food with folic acid for women in the reproductive age group.

 

Accepted:  23/11/2021

Published: 30/11/2021

 

*Corresponding Author

Awopola Ibiebelem Jumbo

E-mail: awopola2002@gmail.com, hernsi@yahoo.com

Phone: +2347064901474

 

Keywords:

Giant Omphalocoele, congenital anomaly, folic acid, prenatal diagnosis.

 

 

 


 

REFERENCES:

 

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11.  Rattan KN, Singh J, Jakhar R, Dalal P, Sonika P (2018). Omphalocele: 15 years experience from a single centre in a developing country. J Clin Neonatol 7: 125-129.

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Cite this Article: Jumbo, AI; Nonye-Enyidah, EI (2021). Giant Omphalocele With Multiple Major Structural Anomalies In A Primipara At 25 Weeks Gestation: A Rare Case Report. Greener Journal of Medical Sciences, 11(2): 246-248.

 


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